Logline: 46 year old, Joel Bentley, is the oldest male living with the rare disease, Lesch-Nyhan Syndrome. This intimate portrait documents a day in the life of this extraordinary human who just so happens to be in a wheelchair. Short Description: Documentary short film, Man with Mittens is an intimate look into the daily life of the oldest man living with Lesch-Nyhan Syndrome. The average life expectancy of those living with this disease is mid-20's; Joel is 46. LNS is extremely rare and stems from a mutation of the X gene on the mother's side. Although documented occurring only in males, there have been 6 cases of females. Lesch-Nyhan is unique in its cruel attributes of uncontrollable self-mutilation, such as head banging and finger biting (sometimes off). Mittens are worn to prevent self-harm and restraints are bound to their wheelchair and bed frame. This documentary is not your talking heads informational film about the disease, rather the man living with the dise...
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